3. Pathways of Amino Acid Degradation
Some Amino Acids Can Contribute to Gluconeogenesis, Others to Ketone Body Formation
Several Enzyme Cofactors Play Important Roles in Amino Acid Catabolism
Six Amino Acids Are Degraded to Pyruvate
Seven Amino Acids Are Degraded to Acetyl-CoA
Phenylalanine Catabolism Is Genetically Defective in Some People
Five Amino Acids Are Converted to α-Ketoglutarate
Four Amino Acids Are Converted to Succinyl-CoA
Branched-Chain Amino Acids Are Not Degraded in the Liver
BOX 18-2 MMA: Sometimes More than a Genetic Disease
Asparagine and Aspartate Are Degraded to Oxaloacetate