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Internal Medicine
Porphyrias
Acute Intermittent Porphyria (AIP)
Path, Acute Intermittent Porphyria (AIP)
Accumulation in nervous tissue Inhibits Action of Gamma Aminobutyric Acid (GABA)
Resulting in Neurotoxicity via Lipid Peroxidation
Causing Autonomic and Peripheral Neuropathy
Axonal neuropathy can lead to:
Can Mimick:
Parents
Axonal neuropathy can lead to:
Children
Guillain-Barré Syndrome